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Table 2 Additional contribution of: positive results in EEG and CSF examination (14.3.3 protein test) to diagnosis of probable sporadic CJD; and identified PrP gene mutation to diagnosis of genetic HTSE.

From: Human transmissible spongiform encephalopathies in eleven countries: diagnostic pattern across time, 1993–2002

Year of death Cases solely with positive EEG
Number and percentage of probable sporadic CJD cases
Cases solely with positive CSF 14.3.3 test
Number and percentage of probable sporadic CJD cases
Cases with mutation and negative or missing data on family history.
Number and percentage of genetic TSE cases
1993 52 (95) - 13 (48)
1994 60 (70) 7 (8) 16 (50)
1995 61 (68) 4 (4) 15 (45)
1996 62 (64) 13 (14) 23 (55)
1997 30 (30) 21 (21) 20 (53)
1998 32 (18) 65 (36) 26 (55)
1999 15 (9) 67 (38) 24 (49)
2000 11 (6) 79 (41) 23 (40)
2001 8 (5) 95 (58) 30 (44)
2002 4 (3) 69 (54) 40 (65)