Table 1 Frequency distribution of the 43 PKU patients
From: Quality of Life (QoL) assessment in a cohort of patients with Phenylketonuria
Variables | Strata | No. (%) | Mean ± SD | Mean ± SD normative population (Child Self-report) | Mean ± SD normative population (Parent proxy-report) |
|---|---|---|---|---|---|
Gender | Female | 20 (46.5) | Â | Â | Â |
Male | 23 (53.5) | Â | Â | Â | |
Age (years) |  |  | 17.09 ± 8.98 |  |  |
Patients | Adult | 17 (40.0) | Â | Â | Â |
Pediatric | 26 (60.0) | Â | Â | Â | |
Education level (pediatric patients) | Nursery | 3 (11.5) | Â | Â | Â |
Primary school | 12 (46.2) | Â | Â | Â | |
Junior secondary school | 11 (42.3) | Â | Â | Â | |
Education level (adult patients) | Secondary school | 14 (82.4) | Â | Â | Â |
Post-graduate | 3 (17.6) | Â | Â | Â | |
Employment status (adult patients) | Student | 5 (29.4) | Â | Â | Â |
Employed | 9 (52.9) | Â | Â | Â | |
Unemployed | 3 (17.7) | Â | Â | Â | |
Treatment type | Diet | 21 (48.8) | Â | Â | Â |
BH4 | 22 (51.2) | Â | Â | Â | |
Treatment length (months) |  |  | 209.65 ± 140.02 |  |  |
QoL pediatric (range: 0-100) |  |  | 79.26 ± 82.97 | 79,37 ± 10 [24] | 81,74 ± 11,21 [24] |
QoL adults (range: 4-20) |  |  | 16.47 ± 0.51 | 14,9 ± 2,9 [26] |  |